The origins of the classification

Theoretical basis for combining these various

diseases in the same group was the fact that their
basis is a preferential loss of connective tissue, as
dense, which include the dermis, tendons, ligaments,
cartilage, bone and others, and its special types
(synovial and serous membranes, basal membranes
of blood vessels and epithelium, etc.).

Working classification and nomenclature of

rheumatic diseases (1999)

I. Rheumatism (rheumatic fever)

II. Diffuse diseases of connective tissue
1.0. Lupus Erythematosus
2.0. Systemic Scleroderma
3.0. Diffuse Fasciitis
4.0. Dermatomyositis (polimiozit)
5.0. Disease hoegren
6.0. Mixed connective tissue disease
7.0. Rheumatic polimialgia
8.0. Recurrent polihondritis, including Tietze disease
9.0. Recurrent pannikulitis (Weber-Christian disease)

 Working

classification and nomenclature of rheumatic

diseases (1999)
III. Systemic Vasculitis
1.0. periarteritis nodosa
2.0. Granulomatous arteritis:

2.1. Wegener's granulomatosis

2.2. Eosinophilic granulomatous vasculitis
2.3. Giant cell arteritis temporal (Horton's disease)
2.4. Nonspecific aortoarteriit (Takayasu's disease)

3.0. Hyperergic angiitis

3.1. Hemorrhagic vasculitis (Henoch disease - purpura)
3.2. Goodpasture's syndrome
3.3. Mixed cryoglobulinemia (cryoglobulinemc purpura)

4.0. Thromboangiitis obliterans (Buerger's disease)

5.0. Behcet's syndrome
6.0. Kawasaki syndrome (muco-cutaneous-glandular syndrome)

Working classification and nomenclature of

rheumatic diseases (1999)

IV. Rheumatoid arthritis

V. Juvenile arthritis
VI. Ankylosing spondylitis (Bechterew)
VII. Arthritis, combined with spondylarthritis
1.0. psoriatic arthritis
2.0. Reiter's disease
3.0. Arthritis in chronic nonspecific bowel disease
(ulcerative colitis, ileitis regionar-ny Crohn's disease)
4.0. Arthritis, and (or) sacroiliitis unspecified
etiology

VIII. Arthritis associated with infection

1.0. infectious arthritis
1.1. Bacterial (staphylococcal, brucellosis, syphilis,
spirochetal, mycobacterial, tuberculosis, etc.)
1.1.1. Lyme disease
1.1.2. Whipple's disease
1.2. viral
1.3. fungal
1.4. parasitic

2.0. Reactive arthritis

2.1. Postenterocolitic (shigellosis, yersiniosis,
salmonellosis, klebsiellosis, etc.)
2.2. Urogenital (excluding Reiter's disease and
gonorrhea)
2.3. After nasopharyngeal infection
2.4. After vaccination

2.0.

2.1. (, , ,
.)

2.2. ( )

2.3.

2.4.

IX. microcrystalline arthritis

1.0. primary gout
2.0. Gout secondary (drug, renal insufficiency,
lead intoxication, etc.)
3.0. Chondrocalcinosis (pseudogout)
4.0. hydroxyapatite arthropathy


(1999)

IX.
1.0.

2.0. (,
,
.)
3.0. ()
4.0.

X. osteoarthritis
XI. Other joint diseases
1.0. palindromic rheumatism
2.0. intermittent hydrarthrosis
3.0. multiple retikulohystiocytosis
4.0. Sinovioma
5.0. chondromatosis of the joint
6.0. Villonodulary synovitis

X.
XI.
1.0.

2.0.
3.0.
4.0.
5.0.
6.0.

XII. Non-rheumatic diseases with arthropathy

1.0. allergic diseases

2.0. Metabolic disorders
2.1. Amyloidosis
2.2. Ochronosis
2.3. Hyperlipidemia
2.4. hemochromatosis
3.0. Congenital defects of the connective tissue metabolism
3.1. Marfan's syndrome
3.2. Desmogenez imperfecta (Ehlers - Danlos syndrome)
3.3. Hypermobility syndrome
3.4. MPS


(1999)

XII.

1.0.
2.0. 2.1. 2.2.
2.3. 2.4.
3.0.
3.1. 3.2.
(
) 3.3. 3.4.

4.0. endocrine diseases

5.0. nervous
6.0. Diseases of the blood
7.0. Paraneoplastic syndrome (malignant tumors of
various sites)
8.0. occupational diseases
9.0. Other diseases 9.1. Sarcoidosis is 9.2. Periodic
disease 9.3. Chronic active hepatitis 9.4.
hypovitaminosis C

 4.0.

5.0.
6.0.
7.0. (
)
8.0.
9.0. 9.1. 9.2.
9.3.
9.4.

XIII. Diseases of the extra-articular soft tissues 1.0.

Diseases of the muscles of
1.1. Myositis
1.2. Ossifitsiruyuschy myositis
2.0. Diseases of the tissues around
3.0. Diseases of the fascia and aponeuroses 4.0,
subcutaneous disease. Fat
5.0. Poliosteoartromialgiya (psychogenic
rheumatism)


(1999)

XIII. 1.0.
1.1. 1.2.
2.0.
3.0.
4.0, .
5.0.
( )

XIV. Bone disease and osteochondropathy

1.0. bone disease
1.1. Osteoporosis (osteopenia), generalized
1.2. osteomalacia
1.3. Osteopathy hypertrophic pulmonary (MarieBamberger syndrome)
1.4. Osteitis deformans (Paget's disease)
1.5. Osteolysis (unspecified etiology)

XIV.
1.0.
1.1.

()
1.2.
1.3. ( )
1.4. ( )
1.5. ( )

2.0. osteochondropathy
2.1. Aseptic necrosis of the femoral head (Perthes
disease) and other sites (Khler's disease I and II,
disease Kenbeka, etc.)
2.2. osteochondritis dissecans
2.3. Osteochondropathy vertebral disease
(Sheyermana - May, Calve's disease)
2.4. Osteochondropathy tuberosity of the tibia
(Osgood disease - Schlatter

2.0.
2.1.

( )
( I II, .)
2.2.
2.3. (
May, )
2.4.
(