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People with McCune-Albright syndrome may have symptoms related to bones,
the endocrine system, or skin. The symptoms can range from mild to severe.

Bone symptoms
Those with McCune-Albright syndrome often have polyostotic
fibrous dysplasia (pronounced pa-lee-oh-STOT-ik FIE-bruss
diss-PLAY-jsha), which occurs when normal bone is replaced by
softer, fibrous tissue. When this happens in weight-bearing bones,
plexiform neurofibromas. cc.oulu.fi

optic glioma. www.fleni.org.ar!


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Lisch Nodules. www.emedicine.com!

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E tiology

The gene for NF1 has been isolated to chromosome 17. The gene product, neurofibromin,
is thought to function as a growth suppressor.

Pathology
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x A.C.- Anterior Communicating Artery.


x A.C.A.- Anterior Cerebral Artery.
x A.I.C.- Anterior Inferior Cerebellar Artery.
x B.- Basilar Artery.
http://www.emedicine.com/asp/image_search.asp?query=Craniopharyngioma

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# hyperpigmentation, epid thicken
STOMACH, LUNG, BREAST, UTERUS Ca
a/w: congenital lipodystrophy
niacin

www.uspharmacist.com
medicine.ucsd.edu

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www.brown.edu
1. Central scotoma resulting from inflammation of the
optic disc

2. Junctional scotoma

3. Bitemporal hemianopia resulting from a lesion around


the optic chiasm

4. Incongruous homonymous hemianopia resulting from


a lesion in the optic tract

5. Homonymous quadrinopia resulting from a lesion in


the temporal lobe

6. Homonymous hemianopia resulting from a lesion in


the occipital lobe.

http://www.mrcophth.com/

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www.emedicine.com
MR venogram - axial view; A = Lateral (transverse) sinus; B = Sigmoid sinus; C =
Confluence of sinus...
!
cavernous sinus www.nature.com
!
!
www.uicomp.uic.edu!
!
www.uicomp.uic.edu!
!
!
www.uicomp.uic.edu!
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