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Fibular hemimelia
Clubfoot
Spinal dysplasia
Facial dysplasia
Agenesis of the cruciate
ETIOLOGY
Maternal ingestion of drugs e.g: Thalidomide
Deficit of
HISTOLOGICAL
Abnormal proliferation of chondrocytes
Abnormal maturation of chondrocytes in proximal
growth zone
Disorganized matrix- inadequate preparation of matrix-
CLASSIFICATION
1.
Aitken's
2.
Pappas
3.
Kalamchi et al
4.
Ainstutz
Dysplastic acetabulum,
Absent femoral head,
Short femur.
segment
Group V- total absence of the femur.
Ainstutz (1969)
Type 1. Congenital short femur with bowing,
coxa vara and normal acetabulum
MANAGEMENT
Basic problems
1.
2.
3.
4.
Treatment
Bilateral PFFD is best treated non-operatively
Treatment is highly individualized -ranges from
Operative Treatment
Hip Stability
subtrochanteric osteotomy
Amputations
Above-the-Knee Amputation
Below knee amputation
ROTATION PLASTY
Described byVan Nes ,
Modified by Kostuik et al.& later by Gillespie & Torode
Arthrodesis of
Ilizarov
Knee arthrodesis
THANK YOU
Thank you